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(In ICD-O-3, behavior will change from /1 to /3 and these cases will be reportable)

9950/3 Polycythemia vera (PV, P. vera)
Definition overproduction of erythrocytes/red blood cells
ICD-9 code 238.4
Synonyms Polycythemia rubra vera
Proliferative polycythemia
Chronic erythremia (ICD-9 207.1)
Primary polycythemia
Splenomegalic polycythemia
Vaquez-Osler disease; Osler-Vaquez disease
9960/3 Chronic myeloproliferative disease, NOS
Definition overproduction of one or more type of blood cell
ICD-9 code 238.7
Synonym Chronic myeloproliferative disorder
9961/3 Myelosclerosis with myeloid metaplasia
Definition condition where bone marrow is initially overactive but then develops fibrosis or scar tissue; term used when myelofibrosis/myelosclerosis is the first disease identified
ICD-9 code 238.7
Synonyms Myelofibrosis as a result of myeloproliferative disease
Megakaryocytic myelosclerosis
Myelofibrosis (idiopathic) with myeloid metaplasia (AMM)
Agnogenic myeloid metaplasia (term commonly used in US; not in ICD-0-3)

Primary myelofibrosis (PMF)> See also acute myelofibrosis (9931/3)
9962/3 Essential thrombocythemia
Definition overproduction of platelets/thrombocytes resulting in circulatory problems
ICD-9 code 238.7
Synonyms Essential thrombocythemia
Essential hemorrhagic thrombocythernia
Idiopathic hemorrhagic thrombocythernia
Primary thrombocythernia
9863/3 Chronic myelogenous leukemia, NOS

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