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There are a number of diagnoses that are malignant
and reportable but do not sound that way.
Atypical carcinoid
SETTLE, CASTLE
Rhabdoid tumor, NOS
Intratubular germ cell neoplasia
Epithelioid trophoblastic tumor
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Mixed pineal tumor, transitional
pineal tumor
Atypical teratoid/rhabdoid tumor
Pagetoid reticulosis
Generalized Langerhans cell histiocytosis
Agnogenic myeloid metaplasia
Acute progressive histiocytosis X
Heavy chain disease
Immunoproliferative small intestinal disease
Hypereosinophilic syndrome
Therapy-related myelodysplastic syndrome
Atypical carcinoid
and typical carcinoid
have different histology codes, and both have behavior codes
of /3.
SETTLE is spindle epithelial
tumor with thymus-like element.
CASTLE is carcinoma
showing thymus-like element.
Rhabdoid tumor is one
of the complex mixed and stromal neoplasms.
Intratubular germ cell neoplasia
is an in situ term that you may recognize from the TNM staging
of testicular cancer.
Epithelioid trophoblastic
tumor is a new code in the hydatidiform mole series.
Mixed and transitional pineal
tumors are in the CNS, as is atypical teratoid/rhabdoid
tumor.
Pagetoid reticulosis
is a synonym for mycosis fungoides.
Generalized Langerhans cell
histiocytosis is predominantly a disease of childhood.
Agnogenic myeloid metaplasia
is a term used in the U.S. as a synonym for myelosclerosis.
Acute progressive histiocytosis
X is a specific type of Histiocytosis X. Histiocytosis
X was a term proposed by Dr. Lichtenstein in 1952 to embrace
three disorders characterized by accumulation of histiocytes
in different tissues: eosinophilic granuloma, Hand-Schuller-Christian
syndrome, and Letterer-Siwe disease.
Heavy chain disease
and immunoproliferative small
intestinal disease are rare tumors that were already
in ICD-O-2.
Hypereosinophilic syndrome
(9964/3) is a new term with a new code and is a chronic myeloproliferative
disorder of the bone marrow (C42.1).
Therapy-related myelodysplastic
syndrome (9987/3) is also a new term with a new code
and also arises in the bone marrow (C42.1).

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